Term
Metaphysis of long bones in kids (<20) grows out like a stalk may progress to ___ |
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Definition
osteochondroma ("extosis")
may progress to chondrosarcoma |
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Term
| in medullary cavity of bones of distal extremities |
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Definition
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Term
many enchondromas
many enchondromas + telangiectasia |
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Definition
Enchondromatosis (Ollier disease)
Maffucci syndrome (increased risk of ovarian & brain tumors) |
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Term
| glistening, malignant mass in medullary cavity. Derived from enchondroma or osteochondroma |
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Definition
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Term
benign osteoblastic tumor <2cm '' >2cm |
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Definition
osteoid osteoma osteoblastoma |
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Term
| things associated w/ gardner syndrome |
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Definition
- APC mutation - Desmoid tumors (deep, intrabdominal fibromatosis) - Osteomas (esp on jaw) - epidermoid cysts - sebaceous cysts |
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Term
| Osteosarcoma most likely patient |
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Definition
| male <20 (second smaller peak in elderly) |
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Term
osteosarcoma risks? typical locations? |
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Definition
male, pagets, avascular necrosis, irradiation, RB, p53
Knee>hip>shoulder>jaw |
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Term
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Definition
| osteosarcoma raises periosteum |
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Term
| soap-bubble on radiography |
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Definition
| giant cell tumor (from lysis, expresses RANK-L) |
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Term
| homer-write pseudorossettes |
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Definition
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Term
| translocation in ewing sarcoma |
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Definition
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Definition
| malignant giant cell tumor |
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Definition
| fibrous histiocytoma (aka dermatofibroma) |
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Definition
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